ADAMTS13
ADAMTS13proteinADAMTS13 deficiency permits ultralarge VWF multimer accumulation, amplifying platelet adhesion and thrombotic risk in acute coronary events.
Pathway placement
Cascade stepEndothelial activation & erosion
Confidencehigh
RationaleVWF multimer-size regulator; endothelial dysfunction marker; imbalance drives platelet hyperadhesion.
Also acts inPlatelet activation
Druggability
DruggableYes
Known drugs / candidates1
Small-molecule tractableYes
Antibody tractableYes
EnsemblENSG00000160323
Type I vs non-Type I discrimination
ScoresIndeterminate
R — rupture / Type-I67
C — non-Type-I48
A — assay feasibility72
E — evidence strength69
T1DI (composite)30
Specificity differential (R−C)+19.1
Non-Type-I axis panel
Does this marker also move in each non-Type-I setting? mag 0–3; higher means less Type-I-specific. n/a = no evidence retrieved, which is not the same as no change.
2sepsis / systemic inflammationn/a
2anemia / acute blood lossmag 3
2hypovolemia / dehydrationn/a
2tachyarrhythmiamag 0
2hypoxemia / respiratory failuren/a
2hypertensive emergencymag 0
2high-demand / peri-operative stressmag 2
3sudden cardiac deathmag 2
4aPCI-related periproceduralmag 1
4bstent thrombosisn/a
4cin-stent restenosisn/a
5CABG-relatedmag 2
Coverage: 7/12 axes with evidence
Tier: deep-scored (abstract-extracted) · 11 supporting references. See the discrimination table for all markers.
Assay & specimen
Validated clinical assay
Specimen
Platelet-poor plasma
Collection tube
Sodium citrate 3.2% (light blue-top)
Method / principle
FRET-based activity assay
Reagent / substrate
FRETS-VWF73 fluorogenic substrate
Platform
Fluorometer / ELISA
Turnaround · availability
Send-out · Reference lab
Literature evidence(4)
- Molecular determinants of thromboinflammatory activation in inflammatory bowel disease.Journal of molecular medicine (Berlin, Germany) · 2026 · PMID 42298010 · doi
- Plasma Interleukin-6 (IL-6), Angiopoietin-2, and C-Reactive Protein Levels Predict Subsequent Type 1 Myocardial Infarction in Persons With Treated HIV Infection.Journal of acquired immune deficiency syndromes (1999) · 2023 · PMID 37018921 · doi
- ADAMTS proteins in human disorders.Matrix biology : journal of the International Society for Matrix Biology · 2018 · PMID 29885460 · doi
- Acute myocardial infarction as a systemic prothrombotic condition evidenced by increased von Willebrand factor protein over ADAMTS13 activity in coronary and systemic circulation.Heart and vessels · 2008 · PMID 18810578 · doi